CASE 408 : DIFFUSE SKIN MACULAR MASTOCYTOSIS, Dr PHAN THANH HẢI, MEDIC MEDICAL CENTER, HCMC, VIETNAM

Baby 6 month old, onset with fever and skin eruption for 3 months, starting in the legs and going to face and full body.  

Itching, in beginning lesion is red skin papula  and  progressing  to macular  shape (see foto of  face,  body).  Dermatologist  represented the lesion with crash and trap which  is  swelling  as  bullus (foto). Darier ‘s sign positive).

Blood tests  are normal .

Ultrasound  of this skin lesion detected  intra dermal hypoechoic infiltration, hypovascular pattern ( US 1, US 2).

Biopsy  of the  skin lesions and  microscopic report with histobiochemistry staining is  MASTOCYTOSIS. So this case is thought  Diffuse skin macular  mastocytosis.